Lymphoid Interstitial Pneumonia

Lymphoid interstitial pneumonia is a rare pulmonary disease, occurring mainly in children. O'Brodovich et al. (1980) reported LIP in 2 brothers, the first and sixth born of 9 sibs from unrelated parents. In the older brother, digital clubbing was noted at age 3 years. Diagnosis was made at age 9. Death from right-sided heart failure occurred at age 12. The younger, aged 13 at the time of report, was living and able to work on the family farm in Manitoba. He also had mild aortic stenosis for which valvulotomy was performed.