Dentin Dysplasia With Sclerotic Bones

Clinical Features

Morris and Augsburger (1977) reported a 4-generation kindred with teeth resembling those in dentin dysplasia type I (125400), also known as radicular dentin dysplasia. The long bones, as well as the maxillary and mandibular alveoli, were more dense than normal, with narrow or occluded marrow spaces and thick cortices. Male-to-male transmission was observed.

Inheritance

The transmission pattern of dentin dysplasia with sclerotic bones in the family reported by Morris and Augsburger (1977) was consistent with autosomal dominant inheritance.