Coenzyme Q10 Deficiency Watchlist (log in to enable) Retrieved 2021-01-18 Source Wikipedia Trials — Genes COQ2, COQ8A, COQ9 Drugs (S)-6-hydroxy-2,5,7,8-tetramethyl-N-((R)-piperidin-3-yl)chroman-2-carboxamide hydrochloride, Alpha-tocotrienol quinone ( VINCERINONE ), Ubiquinol (S)-6-hydroxy-2,5,7,8-tetramethyl-N-((R)-piperidin-3-yl)chroman-2-carboxamide hydrochloride, Alpha-tocotrienol quinone ( VINCERINONE ), Ubiquinol ⋯ Interested in hearing about new therapies? Registered! Coenzyme Q10 deficiency is a deficiency of Coenzyme Q10. It can be associated with COQ2, APTX, PDSS2, PDSS1, CABC1, and COQ9. Some forms may be more treatable than other mitochondrial diseases.