Congenital Self-Healing Reticulohistiocytosis

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Retrieved
2021-01-18
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Congenital self-healing reticulohistiocytosis is a condition that is a self-limited form of Langerhans cell histiocytosis.:720

Symptoms

Non-specific inflammatory response, which includes fever, lethargy, and weight loss. This is suspected of being a genetic disorder, and as the name implies, is self healing.

  • Skin: Commonly seen are a rash which varies from scaly erythematous lesions to red papules pronounced in intertriginous areas. Up to 80% of patients have extensive eruptions on the scalp.
  • Lymph node: Enlargement of the lymph nodes in 50% of Histiocytosis cases.

Diagnosis

Treatment

History

It was first described by Ken Hashimoto and M. S. Pritzkar in 1973.

See also

  • List of cutaneous conditions
  • X-type histiocytosis