Monoamine Oxidase A Deficiency Watchlist (log in to enable) Retrieved 2021-01-23 Source Orphanet Trials — Genes MAOA, F5, SPARC Drugs — Interested in hearing about new therapies? Registered! Monoamine oxidase-A deficiency is a very rare recessive X-linked biogenic amine metabolism disorder characterized clinically by mild intellectual deficit, impulsive aggressiveness, and sometimes violent behavior and presenting from childhood.