Ackerman Syndrome

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Retrieved
2021-01-18
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Ackerman syndrome is a familial syndrome of fused molar roots with a single canal (taurodontism), hypotrichosis, full upper lip without a cupid's bow, thickened and wide philtrum, and occasional juvenile glaucoma. It was described by James L. Ackerman, A. Leon Ackerman, and A. Bernard Ackerman.

It can also refer to interstitial granulomatous dermatitis.

Signs and symptoms

  • Fused molar roots
  • Single root canal
  • Juvenile glaucoma
  • Sparse body hair
  • Distinct facial features: full upper lip, absence of cupid's bow, thick philtrum
  • Syndactyly
  • Increased pigmentation of finger joints
  • Clinodactyly of fifth finger.

Diagnosis

Treatment