Cleft Palate, Deafness, And Oligodontia

In a sibship of Swedish extraction, Gorlin et al. (1971) observed 2 sisters with cleft soft palate, severe oligodontia of the deciduous teeth, no permanent dentition, bilateral conductive deafness due to fixation of the footplate of the stapes, short halluces with wide space between the first and second toes, and coalition of bones in the foot. Gorlin (1989) knew of no further cases.